mitochondrial intermediate peptidase
The information on this page was automatically extracted from online scientific databases.
From NCBI Gene:
The product of this gene performs the final step in processing a specific class of nuclear-encoded proteins targeted to the mitochondrial matrix or inner membrane. This protein is primarily involved in the maturation of oxidative phosphorylation (OXPHOS)-related proteins. This gene may contribute to the functional effects of frataxin deficiency and the clinical manifestations of Friedreich ataxia. [provided by RefSeq, Jul 2008]
Cleaves proteins, imported into the mitochondrion, to their mature size.