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Catabolic process
Catabolic process
ACADM
: acyl-Coenzyme A dehydrogenase, C-4 to C-12 straight chain
ACADS
: acyl-Coenzyme A dehydrogenase, C-2 to C-3 short chain
ACADVL
: acyl-coenzyme A dehydrogenase, very long chain
ADA
: adenosine deaminase
ADAMTS13
: ADAM metallopeptidase with thrombospondin type 1 motif, 13
AGA
: aspartylglucosaminidase
ALDH4A1
: aldehyde dehydrogenase 4 family, member A1
ALDH5A1
: aldehyde dehydrogenase 5 family, member A1
AMT
: aminomethyltransferase
APOE
: apolipoprotein E
ARG1
: arginase, liver
ASL
: argininosuccinate lyase
ASPA
: aspartoacylase (Canavan disease)
ATG16L1
: ATG16 autophagy related 16-like 1 (S. cerevisiae)
AUH
: AU RNA binding protein/enoyl-Coenzyme A hydratase
BARD1
: BRCA1 associated RING domain 1
BCKDHA
: branched chain keto acid dehydrogenase E1, alpha polypeptide
BCKDHB
: branched chain keto acid dehydrogenase E1, beta polypeptide
CLN3
: ceroid-lipofuscinosis, neuronal 3
CPS1
: carbamoyl-phosphate synthetase 1, mitochondrial
CPT1A
: carnitine palmitoyltransferase 1A (liver)
CPT2
: carnitine palmitoyltransferase 2
CUL7
: cullin 7
ERAP1
: endoplasmic reticulum aminopeptidase 1
F12
: coagulation factor XII (Hageman factor)
F2
: coagulation factor II (thrombin)
FAH
: fumarylacetoacetate hydrolase (fumarylacetoacetase)
FLNA
: filamin A, alpha
FOXL2
: forkhead box L2
FUCA1
: fucosidase, alpha-L- 1, tissue
G6PD
: glucose-6-phosphate dehydrogenase
GALE
: UDP-galactose-4-epimerase
GCH1
: GTP cyclohydrolase 1
GLA
: galactosidase, alpha
GLDC
: glycine dehydrogenase (decarboxylating)
GM2A
: GM2 ganglioside activator
HADHB
: hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit
HGD
: homogentisate 1,2-dioxygenase (homogentisate oxidase)
HPD
: 4-hydroxyphenylpyruvate dioxygenase
MAN2B1
: mannosidase, alpha, class 2B, member 1
MCCC1
: methylcrotonoyl-Coenzyme A carboxylase 1 (alpha)
MCCC2
: methylcrotonoyl-Coenzyme A carboxylase 2 (beta)
MMP20
: matrix metallopeptidase 20
MUTYH
: mutY homolog (E. coli)
MYH7
: myosin, heavy chain 7, cardiac muscle, beta
PARK2
: Parkinson disease (autosomal recessive, juvenile) 2, parkin
PRKAG2
: protein kinase, AMP-activated, gamma 2 non-catalytic subunit
PROC
: protein C (inactivator of coagulation factors Va and VIIIa)
PSEN1
: presenilin 1
PSEN2
: presenilin 2 (Alzheimer disease 4)
SERPING1
: serpin peptidase inhibitor, clade G (C1 inhibitor), member 1
SOD1
: superoxide dismutase 1, soluble
SPG7
: spastic paraplegia 7 (pure and complicated autosomal recessive)
TAT
: tyrosine aminotransferase
TMPRSS3
: transmembrane protease, serine 3
UBE3A
: ubiquitin protein ligase E3A
VCP
: valosin-containing protein
VHL
: von Hippel-Lindau tumor suppressor
Source:
Gene Ontology
Consortium
(June 2009).
Published: November 20, 2009